in

Progressive Retinal Atrophy (PRA) - Lisosa & Matšoao

Progressive retina atrophy (eo hape e khutsufalitsoeng ka hore ke PRA) ke lefu la mahlo le futsitsoeng leo butle-butle le lebisang lefung la retina. Lintja tse amehileng li foufala mahlong a mabeli ka nako e telele. Ha ho na mekhoa ea phekolo - ke kahoo liteko tsa lefutso li leng bohlokoa haholo ho tsoalisong ha lintja.

Ho beng ba lintja ba bangata, matšoao a pele a bofofu ba pele a tla e le ntho e makatsang: lintho li lokela ho tsoela pele joang? Hona u entse phoso efe feela? Leha ho le joalo, likotsi kapa mokhoa o fosahetseng oa bophelo hase kamehla o bakang mafu a mahlo. Ka bomalimabe, sesosa sa ho lahleheloa ke pono ka linako tse ling se kenngoa liphatseng tsa lefutso tsa ntja nakong ea tsoalo. Progressive retinal atrophy (PRA) ke sehlopha sa mafu a joalo a liphatsa tsa lefutso a mahlo ao ka bomalimabe a lebisang bofofu bo feletseng ho liphoofolo tse amehileng (lintja le likatse).

Sesosa sa PRA

Joalokaha ho se ho boletsoe, ha ho na lisosa tse ka ntle tsa tsoelo-pele ea retinal atrophy. Mafu ana a mahlo a futsa liphoofolo tse amehileng, 'me, ho itšetlehile ka mofuta oa lefu lena, a ka hlaha ha malinyane a sa le monyenyane. Ho lintja, lefu lena le fumanoa ka har'a liphatsa tsa lefutso tsa mefuta e mengata ea lintja, likatse, mefuta ea Somalia le Abyssinian e ameha haholo. Maemong a mangata, ke mofuta oa autosomal recessive o ka bakang PRA. Sena se bolela hore ha ho hlokahale hore ntjanyana e be le PRA haeba e mong oa batsoali a e-na le lefutso.

Leha ho le joalo, ho mastiffs, lefutso le futsitsoe haholo, 'me ho Husky ea Siberia le Border Collie, lefutso le hokahane le X chromosome. Mefuta e fapaneng ea liphatsa tsa lefutso tse jereng PRA e etsa hore lipatlisiso le nts'etsopele ea tlhahlobo ea liphatsa tsa lefutso li be thata. Ho se ho ntse ho na le lisebelisoa tsa tlhahlobo tse sebetsang bakeng sa mofuta oa ntja oa Irish Setter, Welsh Corgi Pembroke, Sloughi, Bull Terrier, Mastiff le Bullmastiff. Ka hona, balisa ba nang le botumo bo botle ba mefuta ena ea lintja ba lokela ho lula ba khona ho fana ka setifikeiti sa hore na liphoofolo tse motsoali ke tsona tse tsamaisang liphatsa tsa lefutso kapa che.

Tsela ea Boloetse

Progressive retinal atrophy, joalo ka ha lebitso le bolela, e ama retina ea leihlo. Retina e bopa karolo e ka hare-hare ea fundus ea leihlo, eo ho eona lisele tsa photoreceptor tseo e leng tsa bohlokoa bakeng sa pono, lithupa le likhoune, li kenngoeng. Lithupa li na le boikarabelo ba ho khetholla pakeng tsa leseli le lefifi (pono ea bosiu), 'me ka lebaka la li-cones, mebala e ka khetholloa (pono ea letsatsi). Ho PRA, retina ena le lisele tsa photoreceptor tse kentsoeng ho eona li qala ho shoa hang ha phatsa ea lefutso e qala. Sena se tšoaea qaleho ea bofofu bo feletseng bo tsoelang pele butle-butle. Maemong a mangata, melamu e senyeha pele, e lebisang bofofu bosiu. Ka mor'a moo, li-cones le tsona lia senyeha, 'me lintja tse amehileng ha li sa khona ho bona esita le motšehare.

Matšoao a Pele le Matšoao

Kaha lefu la ho fokola ha retina le tsoela pele butle, hangata le fumanoa ka mor'a nako. Matšoao a pele a atisa ho hlaha pakeng tsa selemo se le seng ho isa ho tse tšeletseng 'me a kenyelletsa feela bofofu bo tloaelehileng bosiu. Sena se bolela hore lintja li tsamaea ka hloko haholo le ka mokhoa o sa tsitsang, haholo-holo bosiu. Ho phaella moo, lens opacities (eo hape e bitsoang cataracts kapa cataracts) e ka boela ea etsahala ka har'a leihlo. Ka mor’a moo, pono ea lintja tsa motšehare le eona ea senyeha, ’me qetellong, li foufala ka ho feletseng mahlong a mabeli. Ka bomalimabe, PRA e lula e ama mahlo ka bobeli. Electroretinography (ERG) ke tsela e molemohali ea ho ngolisa liphetoho ho retina. Bokhoni ba motlakase ba li-neuronal impulses tsa lisele tsa photoreceptor bo lekanyetsoa ho fumana hore na li ntse li sebetsa.

Boprofeta: Na Progressive Retinal Atrophy ke Qetello?

Ka bomalimabe, ha ho na mokhoa oa ho phekola atrophy ea retinal e tsoelang pele kapa ho boloka mahlo a lintja tse kulang. Ho nka khato khahlanong le mafu ana a mahlo, ka hona ho bohlokoa haholo ho beha liphoofolo tse ngata tse tsoalisang tlhahlobo ea liphatsa tsa lefutso ka hohle kamoo ho ka khonehang - ha feela sena se le teng bakeng sa mofuta, ehlile. Ena ke eona feela tsela ea ho netefatsa hore PRA e ka etsahala hanyane le hanyane khafetsa.

Leha ho le joalo, bofofu bo felletseng ha bo bolele ho fela ha lefatše! Lintja tse foufetseng li ka boela tsa phela bophelo bo tletseng le bo thabileng haeba u ela hloko mefokolo ea bona ea pono. Joaloka moetapele oa lifofu, u lokela ho ela hloko litlhoko tse khethehileng tsa liphoofolo, ka mohlala, u li behe holim'a leash ka nako e khutšoanyane le ho ba lemosa ka litšitiso. Ntho ea bohlokoa ka ho fetisisa bakeng sa lintja tse foufetseng ke botsitso - sena se bolela hore u lokela ho qoba ho hlophisa bocha likamore kapa thepa ea ka tlung ha ho khoneha. Hobane haholo-holo maboteng a hau a mane, esita le lintja tse sa boneng li fumana tsela ea tsona ho pota-pota ka mokhoa o makatsang. Ho bapala le lintja tse ling ho ntse ho khoneha - hafeela lintja tse ling li nahanela 'me motsoalle oa hao ea maoto a mane a bonahala a thabela ho sebelisana.

Ho na le mehlala e mengata e meholo ea lintja tse makatsang tse phelang bophelo ba tsona ka botlalo ho sa tsotellehe bofofu ba tsona!

Mary Allen

ngotsoeng ke Mary Allen

Lumela, ke 'na Maria! Ke hlokometse mefuta e mengata ea liphoofolo tse ruuoang lapeng ho kopanyelletsa le lintja, likatse, likolobe, tlhapi, le lidrakone tse litelu. Ke boetse ke na le liphoofolo tse ruuoang lapeng tse leshome hajoale. Ke ngotse lihlooho tse ngata sebakeng sena ho kenyelletsa mokhoa oa ho etsa, lingoliloeng tsa tlhahisoleseling, litataiso tsa tlhokomelo, litataiso tsa mefuta, le tse ling.

Leave a Reply

Avatar

aterese ya hao ya imeile ke ke ho phatlalatswa. masimo hlokahala di tšoauoa *